MRI in Primary Intestinal Lymphangiectasia: A Diagnostic Tool and to Delineate Localization of Involvement
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چکیده
منابع مشابه
MRI in Primary Intestinal Lymphangiectasia: A Diagnostic Tool and to Delineate Localization of Involvement
Intestinal lymphangiectasia (IL) is a rare protein losing enteropathy caused by congenital malformation or obstruction of the intestinal lymphatic drainage system [1]. Elevated pressure in the intestinal lymphatic system causes dilatation and rupture of the lacteals, with loss of lymphatic fluid which is rich in fat and protein. Consequently the clinical features of diarrhea, growth retardation...
متن کاملPrimary intestinal lymphangiectasia.
Primary intestinal lymphangiectasia (PIL) is a rare disease of intestinal lymphatics presenting with hypoproteinemia, bilateral lower limb edema, ascites, and protein losing enteropathy. We report a series of 4 children from Chennai, India presenting with anasarca, recurrent diarrhea, hypoproteinemia and confirmatory features of PIL on endoscopy and histopathology.
متن کاملA Case of Primary Intestinal Lymphangiectasia
A 26-year-old male patient who had an 8 years history of recurrent peripheral edema with diarrhea and hypoproteinemia was evaluated. Endoscopic jejunal and ileal biopsy revealed markedly dilated mucosal lymph vessels with no evidence of inflammation. 99mTc-labeled human serum albumin (HSA) scintigraphy showed significant activity accumulating in the gastrointestinal tract to represent 99mTc-HSA...
متن کاملprimary intestinal lymphangiectasia
primary intestinal lymphangiectasia (pil) is a rare disease of intestinal lymphatics presenting with hypoproteinemia, bilateral lower limb edema, ascites and protein-losing enteropathy. we report a case of pil in a 22 year old patient from tabriz, iran who presented with anasarca edema, recurrent diarrhea, hypoproteinemia and confirmatory features of pil on endoscopy and histopathology. therefo...
متن کاملPrimary intestinal lymphangiectasia (Waldmann's disease)
Primary intestinal lymphangiectasia (PIL), Waldmann's disease, is a rare disorder of unknown etiology characterized by dilated intestinal lacteals leading to lymph leakage into the small-bowel lumen and responsible for protein-losing enteropathy leading to lymphopenia, hypoalbuminemia and hypogammaglobulinemia. PIL is generally diagnosed before 3 years of age but may be diagnosed in older patie...
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ژورنال
عنوان ژورنال: Gastroenterology & Hepatology: Open Access
سال: 2016
ISSN: 2373-6372
DOI: 10.15406/ghoa.2016.05.00137